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Congenital self-healing reticulohistiocytosis

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Title: Congenital self-healing reticulohistiocytosis  
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Language: English
Subject: X-type histiocytosis
Publisher: World Heritage Encyclopedia

Congenital self-healing reticulohistiocytosis

Congenital self-healing reticulohistiocytosis (also known as "Hashimoto–Pritzker disease,"[1] and "Hashimoto–Pritzker syndrome"[2]) is a condition that is a self-limited form of Langerhans cell histiocytosis.[2]:720


Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

  • Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
  • Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.[3]

See also


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